Published on:
    Journal of Cardiovascular Disease Research, 2013; 4(4):239-241
    Short Communication | doi:10.1016/j.jcdr.2014.01.002

    Pulmonary hypertension due to presence of isolated partial anomalous pulmonary venous connection: A case report

    Authors:

    Tarun Kumar, Soumya Patra*, Rangaraj Ramalingam, Navin Agrawal, Ashish Agarwal, Cholenahalli Nanjappa Manjunath

    Department of Cardiology, Sri Jayadeva Institute of Cardiovascular Sciences & Research, Bangalore, Karnataka 560069, India

    Abstract:

    Anomalous pulmonary venous return is an uncommon congenital malformation which can be broadly categorized into partial or total, of which the former is more common. The anomaly is considered to be partial if some of the pulmonary veins drain into the systemic circulation and total if all the pulmonary veins drain into systemic circulation. Isolated partial anomalous pulmonary venous return (PAPVC) is an uncommon finding and is a very uncommon cause of pulmonary arterial hypertension. Whilst many patients with PAPVC remain asymptomatic, some may present at a later age with symptoms related to left-to-right shunt, pulmonary hypertension and right heart failure. We are presenting an interesting case report of an 18 years old patient who presented with exertional dyspnea and fatigue conforming to NYHA class II symptom status. Trans-esophageal echocardiography revealed isolated obstructive PAPVC as the cause for pulmonary hypertension without other demonstrable left-to-right shunts.

    Key words: Partial anomalous pulmonary venous, connection, Pulmonary hypertension, Trans-esophageal echocardiography.