This article reports a rare case of coarctation of the aorta associated with DandyeWalker variant in a 17- year-old girl. Differential diagnoses of coarctation of the aorta and Dandye-Walker variant are extensively discussed. In addition, standard surgical treatment of coarctation as well as new approaches such as endovascular stenting are described in detail to provide therapeutic insights into her management. Although surgical or endovascular repair of coarctation results in significant improvement of systemic hypertension and is associated with better survival, cardiovascular complications are still very common. Thus, long-term follow-up after repair is required, and high-quality imaging studies such as echocardiography, CT and MRI are warranted.
Key words: Coarctation of the aorta, DandyeWalker variant, Hypertension, Surgical repair, Endovascular stent.