Shone’s complex is a Congenital Heart Disease (CHD), consisting of multiple levels of left sided obstructive lesions including supravalvular mitral membrane (SVMM), parachute mitral valve, subaortic stenosis and coarctation of aorta. Cortriatriatum sinister is a rare congenital defect in which a membrane divides LA into two distinct chambers. These two congenital malformations are rare and their occurrence together is still rarer. We report a 1 year 3 month old male baby with h/o failure to thrive, recurrent Respiratory Tract Infection & developmental delay. Presented with rarer combination of shone’s complex and cortriatriatum sinister.
Key words: Shone’s complex, Cortriatriatum sinister, Congenital Heart Disease, 2DEchocardiography, Cortriatriatum dexter